Superior Semicircular Canal Dehiscence: Demonstration with Three-Dimensional Multidedector Ct and Mr Imaging

Introduction: Semicircular canal dehiscence (SCD) syndrome has been defined as a bone defect in the roof of the superior, posterior and lateral semicircular canals. We reported that three-dimension CT and MR imaging of superior SCD is rare in english literature. Case presentation: A 6-year-old boy patient presented with hearing loss and left facial nerve paresis since birth. CT and MR images demonstrated superior SCD causing congenital hearing loss. Discussion: Multidedector CT with multiplanar reconstruction and three-dimension volume rendered imaging is an excellent imaging method to detect this defect. MR imaging should be preferred in the demonstration of the cranial nerves and relationship of SCD with the epidural space in more detail. In conclusion, superior SCD should be considered for differential diagnoses in patients presenting with congenital hearing loss.